Budd-Chiari Syndrome Disorder
Details of the Patient
- Patient’s Name: Unknown
- Patient’s Age: 13
- Patient’s Gender: male
Symptoms shown by the Patient
- ● Huge Splenic Aneurysm (around 7 cm)
- ● Multiple episodes of upper GI bleeding in last 5-6 years
- ● Had developed cirrhosis and has huge collaterals
- ● Due to such spleen, he has developed symptoms of hypersplenism (low platelet count, Low Hemoglobin, and low white cell count)
An Overview of the Case
Master X was diagnosed with Budd Chiari syndrome at age six years. He had multiple episodes of upper GI bleeding in the last 5-6 years. He had developed cirrhosis and had huge collaterals (veins that can bleed).
The patient had a huge spleen reaching up to his right side. The size of the spleen was 27 cm. Due to such a large spleen, he developed symptoms of hypersplenism. like –
- Low platelet count
- Low Hemoglobin
- Low white cell count
The large splenic aneurysm was a serious reason to worry. Any rupture of splenic aneurysm can be catastrophic. Because of collaterals, low platelet count, and such a big aneurysm, operating was a technical challenge.
Luckily, the patient was able to tolerate the surgery very well. The excision of the aneurysm and spleen went very well without any blood loss. The weight of the spleen was more than 2.5 Kg.
Treatment Provided to the Patient
Medical Tests Performed
- Routine CT scan
- Blood platelet count