Liver Transplant in India

Budd-Chiari Syndrome Disorder

Details of the Patient

  • Patient’s Name: Unknown
  • Patient’s Age: 13
  • Patient’s Gender: male

Symptoms shown by the Patient

  • ● Huge Splenic Aneurysm (around 7 cm)
  • ● Multiple episodes of upper GI bleeding in last 5-6 years
  • ● Had developed cirrhosis and has huge collaterals
  • ● Due to such spleen, he has developed symptoms of hypersplenism (low platelet count, Low Hemoglobin, and low white cell count)

An Overview of the Case

Master X was diagnosed with Budd Chiari syndrome at age six years. He had multiple episodes of upper GI bleeding in the last 5-6 years. He had developed cirrhosis and had huge collaterals (veins that can bleed). 

The patient had a huge spleen reaching up to his right side. The size of the spleen was 27 cm. Due to such a large spleen, he developed symptoms of hypersplenism. like –

  • Low platelet count
  • Low Hemoglobin
  • Low white cell count

The large splenic aneurysm was a serious reason to worry. Any rupture of splenic aneurysm can be catastrophic. Because of collaterals, low platelet count, and such a big aneurysm, operating was a technical challenge.

Luckily, the patient was able to tolerate the surgery very well. The excision of the aneurysm and spleen went very well without any blood loss. The weight of the spleen was more than 2.5 Kg. 

Treatment Provided to the Patient

  • surgery

Medical Tests Performed

  • Routine CT scan
  • Blood platelet count

Feedback from the Patient

The surgery saved the life of Master X. He became fit in few days right after the surgery. Now, after the complete recovery, he can lead a healthy life. His parents were also pleased with the treatment.